Background:Esophageal leiomyomatosis is rare with an incidence that is essentially unknown with only a few reported cases. Characteristically there is proliferation of smooth muscle cells in the esophageal wall causing localized circumferential thickening. Esophageal leiomyomas are usually very slow growing and often asymptomatic. Symptomatic tumors are usually greater than five centimeters in diameter. The accepted treatment for esophageal leiomyomatosis ihas been surgical removal, which frequently requires esophagectomy with reconstruction.Case Report:We report a case of a 29-year-old woman with esophageal leiomyomatosis whose presentation was not typical and magnetic resonance imaging proved diagnostic. This patient was effectively with enucleation of the tumor.Conclusions:Recommended treatment for this condition has been total esophagectomy with reconstruction, but we report a case treated with enucleation of the tumor.

Keywords: Leiomyomatosis - diagnosis, Leiomyomatosis - surgery