We present a case of 3.5-year-old boy with echocardiographic and angiographic diagnosis of total anomalous left pulmonary vein drainage; without intracardiac defects. Superior lobe veins diverted blood to the drainage area of superior caval vein, while short veins of inferior lobe joined immediately the coronary sinus. The vein diverting blood from superior lobe was grafted to left atrial auricle through left-side thoracotomy approach, without extracorporeal circulation. Due to unfavourable anatomy of the anomaly and the episode of 10-minute supraventricular tachycardia (associated with the distension of left atrial wall as a result of anastomosis produced), partial correction was considered sufficient, and the connections between left inferior lobe veins and coronary sinus were maintained. Post-operative course was uneventful.

Keywords: treatment, Diagnosis, Abnormalities, Pulmonary Veins